Erythema elevatum diutinum–associated with loss of the uvula

EED: Erythema elevatum diutinum LCV: Leukocytoclastic vasculitis INTRODUCTION Erythema elevatum diutinum (EED) is a rare, chronic form of leukocytoclastic vasculitis (LCV) that belongs to the group of neutrophilic dermatoses including Behçet disease, Sweet syndrome, and pyoderma gangrenosum. The exact pathogenesis of the condition is poorly understood, but it is thought to result from immune complex deposition in small vessels, possibly triggered by an unknown antigen. Importantly, EED is often associated with underlying conditions such IgA gammopathy, and HIV; thus, it is crucial that patients be appropriately screened for these conditions.